Desmoplastic Small Round Cell Tumor of the testis: A rare tumor at an uncommon location

Abstract

Abstract Desmoplastic Small Round Cell Tumor (DSRCT) is an aggressive neoplasm that classically grows in the peritoneal cavity and has poor prognosis. We describe a 13-year-old boy with testicular DSRCT, treated with orchiectomy and chemotherapy who is free of disease 102 months after diagnosis. This is the fifth case of primary DSRCT of the testis described in literature. Moreover, we present a literature review of 28 cases of testicular and paratesticular DSRCT.