PROGRESSION OF PULMONARY ALVEOLAR MICROLITHIASIS TO PULMONARY HYPERTENSION AND COR PULMONALE

Abstract

RONAK SHAH AND PAUL STRACHAN W E D N E S D A Y F E L L O W S C A S E R E P O R T P O S T E R S INTRODUCTION: Pulmonary alveolar microlithiasis (PAM) is a rare disease with less than 600 cases described in the literature. It is characterized by accumulation of calcium phosphate in the alveolar space. (1) Radiographic features are pathognomonic but clinical manifestations are non-specific. We present a case of PAM with progressive deterioration over 20 years leading to pulmonary hypertension (pHTN) and cor pulmonale.