A MULTIDISCIPLINARY APPROACH TO THE TREATMENT OF MALIGNANT HEART TUMOR

Abstract

Introduction : paragangliomas are rare neuroendocrine neoplasms with a frequency of 0.001–0.01% in population, which arise from the adrenal medulla and extrarenal autonomic paraganglia, respectively. Paragangliomas of the heart are extremely rare primary neuroendocrine tumors of the heart, accounting for less than 1% of all cardiac neoplasms. Their location is clinically important as they can interfere with heart function. For large paragangliomas of the heart with myocardial invasion, the need for heart reconstruction or transplantation may potentially arise. Discussion : in our case, taking into account the secretion of catecholamines, sick sinus syndrome, a high risk of bleeding, and tumor fragmentation, the first stage was to achieve the regression of the tumor by means of embolization of heart tumor suppliying afferent with coils. However, due to several sources of blood supply of newgrowth, this method of treatment did not lead to the desired effect. In this regard, the tactics of open surgical intervention was chosen to remove the newgrowth with the reconstruction of heart chambers. According to the data of postoperative biopsy, removed tumor was paraganglioma. Conclusion : this experience shows the importance of a multidisciplinary and personalized approach in treatment of patients in a multidisciplinary hospital.