International Journal of Clinicopathological Correlation | 2019
Karyomegalic tubulointerstitial nephritis with primary focal segmental glomerulosclerosis in a young female: A rare form of steroid-nonresponsive nephrotic syndrome
Abstract
Karyomegalic interstitial nephropathy (KIN) is a rare form of chronic tubulointerstitial nephritis initially described as a familial nephropathy in adults. We present a case of KIN with focal segmental glomerulosclerosis in a 15-year-old young female who became late nonresponder and resistant to steroid therapy. To our knowledge, only one case has been reported in literature.