Sturge–Weber Syndrome: Roots to a Cure a Nightmare in Pediatric Dentistry

Abstract

Abstract Aim and objective This article aims to report a case of Sturge–Weber syndrome (SWS) in a pediatric patient and its systematic dental management to add to the existing literature. Background Sturge–Weber syndrome is one of the vascular disorders, known for its stupendous scope of clinical manifestations and life-threatening complications. The substantial prevalence of oral manifestations in SWS makes it crucial to have a comprehensive knowledge of this rare congenital disorder. Case description This case report represents a case of SWS in an 11-year-old boy with oral, ocular, and neurological features who reported due to pain, unilateral gingival enlargement associated with spontaneous bleeding in the mandibular left region. A multidisciplinary team approach having comprehensive knowledge regarding such rare congenital disorder is a must to prevent its life-threatening complications. Conclusion Sturge–Weber syndrome often affects the oral cavity through vascular lesions. Hence, deep knowledge is immensely important to provide an appropriate dental treatment without complications. Clinical significance Port-wine stains should not be considered as just birthmarks and should be further investigated for its systemic involvement to arrive at a confirmatory diagnosis and treated accordingly with special precautions. How to cite this article Mapara PN, Taur SM, Hadakar SG, et al. Sturge–Weber Syndrome: Roots to a Cure a Nightmare in Pediatric Dentistry. Int J Clin Pediatr Dent 2021;14(1):145–148.