Family of Three Generations with Incontinentia Pigmenti

Abstract

Incontinentia pigmenti, (IP) also known as Bloch-Sulzberger syndrome, is an uncommon X-linked dominantly inherited syndrome, characterized by various cutaneous manifestations which include vesicular, verrucous and pigmented lesion, associated with developmental defects of the central nervous system, skeletal system and the eye.1 We are presenting a family of three generations with Incontinentia Pigmenti and a brief review of clinical updates.