Pleomorphic adenoma of orbital ectopic lacrimal gland associated with swollen optic disc

Abstract

Introduction: Pleomorphic adenoma is the most common benign epithelial neoplasm of the lacrimal gland. This is the case report of a 63-year-old lady with pleomorphic adenoma of ectopic lacrimal gland in the superomedial part of orbit. Case Report: A 63-year-old lady presented with gradually increasing non-axial proptosis of left eye for two years duration. There was downwards and outwards displacement of left eye ball by a hard, palpable mass in the superomedial part of left orbit. The left eye showed relative afferent pupillary defect and swollen optic disc. Computerized tomography demonstrated an extraconal, well-circumscribed mass lesion occupying superomedial part of the left orbit. Complete surgical excision of tumor was performed through anterior orbitotomy. The histopathology showed an encapsulated tumor composed of nests and strands of cuboidal-shaped epithelial cells and myoepithelial cells supported by loose myxoid and hyalinized calcified stroma. The mass was diagnosed “a pleomorphic adenoma arising from ectopic lacrimal gland.” Conclusion: To Zin May Htoon1, Ko Ko Thant1, Le’ Shwe Zin2, Thet Naing3 Affiliations: 1Consultant Ophthalmologist, Department of Ophthalmology, North Okkalapa General and Teaching Hospital, Yangon, Myanmar; 2Consultant Pathologist, Department of Pathology, Yangon General Hospital, Yangon, Myanmar; 3Resident Physician, Department of Ophthalmology, National University Hospital, Singapore, [email protected]. Corresponding Author: Zin May Htoon, Department of Ophthalmology, North Okkalapa General and Teaching Hospital, North Okkalapa Township, Yangon, Myanmar; Email: [email protected] Received: 04 June 2019 Accepted: 05 August 2019 Published: 23 August 2019 PEER REVIEWED | OPEN A CE S our knowledge, this is the first case of extraconal orbital pleomorphic adenoma arising from ectopic lacrimal gland associated with signs of optic neuropathy.