Wong-Type Dermatomyositis: An Extremely Rare Disease in Childhood.

Abstract

Some cutaneous manifestations can hide systemic symptoms of dermatomyositis (DM). The Wong-type dermatomyositis (W-DM) should be considered in the differential diagnosis in children with overlapping symptoms of DM and pityriasis rubra pilaris (PRP). This rare form of DM is reported in only 27 cases in the literature: 6 cases of pediatric age and only 3 with associated cutaneous features of PRP (2 females aged 1 and 18 years and a 12-year-old boy) [1]. Our patient was the fourth case of W-DM with associated cutaneous features of PRP and the first under the age of 10 years. Punch biopsy and knowledge of rare diseases improve the diagnostic ability and therapy. Differential diagnosis includes lupus erythematosus, PRP, and psoriasis. We wish to draw attention to an extremely rare condition in children and, through the clinical images, we highlight the peculiarity of this rare form of DM. Case Presentation