A. Oubaaz

Bilateral enucleation avoided by excision with mitomycin C for bilateral infiltrating conjunctival squamous cell carcinoma in a girl with xeroderma pigmentosum

Xeroderma pigmentosum (XP) was first described by Hebra and Kaposi in 1874. Patients having this condition in early childhood present a photophobia, a photosensitivity, cutaneous pigment changes, and a predisposition for malignancy in sun-exposed mucocutaneous areas and ocular structures. XP patients have a defect in DNA repair related to the nucleotide excision repair pathway or a bypass polymerase pathway. In this paper, we are reporting the case of an eleven-year-old girl presenting a bilateral infiltrating squamous carcinoma of conjunctiva whom we treated with conservative surgery and mitomycin C.

Rapid effect of depletive lumbar puncture on papilledema in intracranial hypertension

A 32-year-old man presented with a 3-month history of chronic headache with transient visual obscurations. Neurological examination was normal. Ophthalmic examination revealed bilateral papilledema with macular serous detachment in both eyes (Fig. 1). Visual acuity was 9/10 in each eye. Neuroimaging and MR venography were normal. Lumbar puncture in the lateral decubitus position found cerebrospinal fluid (CSF) opening pressure of 50 cm H2O, with normal CSF constitution. According to revised diagnostic criteria for the pseudotumor cerebri syndrome [1], diagnosis of idiopathic intracranial hypertension was made. puncture, papilledema resolved (Fig. 2). However, edema restored gradually to its original state within 10 days. Since no aggravation of the vision loss occurred after six months follow-up, surgery (CSF diversion or optic nerve sheath fenestration) has not been offered to patient [2]. Papilloedema refers to swelling of the intraocular (prelaminar) portion of the optic nerve head and in idiopathic intracranial hypertension, it takes place as a result of elevated intracranial pressure, transmitted via the CSF, in the confines of the retrobulbar optic nerve sheath [2]. CSF removal allows a decrease of the intracranial pressure

Macular scar secondary to congenital toxoplasmosis

A 8 years old girl suffers from strabismus since her first months of life. Her visual acuity was very low and could only see fingers moving in her left eye. Her left eye fundus showed a chorioretinal scar in the macula due to congenital toxoplasmosis. The biological findings proved the diagnosis of congenital toxoplasmosis. Functional prognosis of macular scars is very dark.

Les uvéites de l’enfant : à propos de 10 cas

Introduction: Uveitis in children is rare: 3%-8% of all cases. It requires the same diagnostic and etiological processes as uveitis in adults, with additional difficulties at examination and a sometimes insidious progression. Material and methods: Retrospective study of 20 cases of childhood uveitis from 1995 to 2000. All patients received an ophthalmologic examination and an etiological search, with specific and/or symptomatic treatment and follow-up lasting from 6 months to 5 years. Results: The 20 children presenting uveitis were 4-16 years old, with etiologies as follows: 8 cases of Behçet’s disease, 2 cases of Vogt-Koyanagi-Harada’s disease, 1 case of sarcoidosis, 1 case of uveitis associated with coeliac disease, 1 case of toxoplasmosis, 1 case of sympathetic ophthalmia, 1 case of uveitis with streptococcal infection, 3 cases of ocular toxocarosis, and 2 cases with unknown etiology. Treatment based on the etiological findings was started in the cases of toxoplasmosis and uveitis from streptococcal infection. The others were treated with highand then digressive-doses of corticosteroids. Analysis: We have noted the high incidence of Behçet’s disease in our series. Progression was marked by frequent recurrence for one case of Vogt-Koyanagi-Harada’s syndrome and one case of toxoplasmosis. This study also revealed a few cases of complicated cataract. Discussion: Clinical characteristics, diagnosis, and treatment of uveitis in children are discussed.

Maladie de Best compliquée de néovascularisation choroïdienne chez un enfant

INTRODUCTION Bests disease is a progressive macular dystrophy, beginning either in childhood or adolescence. CASE STUDY We report a rare case of choroidal neovascularization complicating vitelliform dystrophy in a child of 8 years with bilateral progressive loss of visual acuity. The ophthalmoscopic examination showed vitelliform lesions in both foveas. Fluorescein angiography confirmed a subretinal neovascular membrane in the left eye. Additional testing also confirmed the diagnosis of Bests disease associated with choroidal neovascularization. DISCUSSION Bests vitelliform macular dystrophy is often asymptomatic because visual acuity tends to remain stable for a long time. A sudden loss of vision suggests the occurrence of complications, such as choroidal neovascularization.

Rétinopathie ischémique chronique bilatérale : à propos d’un cas ☆

La sténose de l’artère carotidienne est définie par une réduction de la lumière par une plaque d’athérosclérose, artérite, ou une dysplasie fibromusculaire. Son incidence est élevée et représente 10 % de la population âgée de plus de 60 ans. Le syndrome d’ischémie oculaire (SIO) chronique, appelée rétinopathie hypotensive, est une forme rare et sévère d’ischémie des segments antérieurs et postérieurs de l’œil secondaire à une sténose sévère ou d’occlusion de l’artère carotidienne.