El Hassane Kabiri

Monostotic fibrous dysplasia of the ribs

Fibrous dysplasia (FD) is a sporadic benign skeletal disorder that can affect one bone (monostotic form) or multiple bones (polyostotic bone). Around 6-20% of monostotic FD occurs in the ribs. The objective of this study was to report our experience in the management of the monostotic FD of the ribs. Between January 2004 and December 2009, seven cases of FD of the rib (six men and one woman, mean age 30.4 years, range 17-40 years) were operated on. The patients were evaluated with plain radiographs and computer tomography (CT). All our patients were symptomatic; two patients presented chest pain and swelling and other patients presented only chest pain. One rib was involved in all our patients (monostotic form): the site was fifth rib (four cases), sixth rib (two cases) or second rib (one case). Radiologically, plain films and CT showed an expansible lesion with a ground-glass centre and thinning of the cortex. Rib resection was performed in all patients; there were no postoperative complications and no recurrence in all cases at mean 43 month follow-up. In symptomatic monostotic FD of ribs, the involved segment of bone may be excised to rule out malignancy and for painful lesions.

Mediastinal hydatid cyst.

Background: The objective of this study was to report our experience in the management of hydatid cysts of the mediastinum. Methods: Among 206 patients who underwent surgery in our department for intrathoracic hydatid cysts between September 2001 and September 2008, 7 patients (3.4%) aged 24 to 49 years (mean, 36.2 years) had mediastinal hydatid cysts. Imaging consisted of chest X‐ray and computed tomography. Surgical approach was by posterolateral thoracotomy in all cases. Results: The cyst was located in the posterior mediastinum in 3 cases (42.8%), in the anterior mediastinum in 2 cases (28.5%) and in the middle mediastinum in 2 cases (28.5%). Two patients had cysts in other thoracic locations (diaphragm, pleural). All cysts were intact. Surgical approach was right thoracotomy in 5 patients (71.4%) and left thoracotomy in 2 patients (28.5%). In 5 cases, a small part of the cyst wall intimately adherent to vital structures was left in place. There were no postoperative complications or mortality. Conclusion: Mediastinal hydatid cyst is an uncommon disease. Because of the surrounding vital structures, the cyst should be removed immediately. Surgical removal remains the treatment of choice for mediastinal echinococcosis, without extensive resection when progression of dissection is impossible or dangerous.

Primary Hydatid Cyst of the Posterior Mediastinum

Hydatid cystic disease is still a health problem in Morocco. Mediastinal localization is very rare. We report the case of a 24-year-old man who presented with right chest pain and dyspnea. Chest X-Ray and computed tomography showed a mediastinal mass. The diagnosis was confirmed perioperatively by macroscopic and histologic investigations. Resection of the cyst was performed, and a small part intimately adherent to the inferior vena cava and oesophagus was left in place. There were no complications or recurrence.

Parietal pleura lipoma : a rare intrathoracic tumor

Lipoma is a common benign tumor of soft tissues in adults. An intrathoracic location, particularly in the parietal pleura, is rare. We report two cases of pleural parietal lipoma with a review of literature. A preoperative diagnosis was established histologically by fine-needle aspiration in the first case and radiologically by computed tomography scan in the second. Both patients underwent surgical excision via thoracotomy and video-assisted thoracic surgery. Pathology examination confirmed the diagnosis of lipoma. The authors emphasize the necessity of surgical resection because of preoperative diagnostic difficulty of discerning lipoma from well-differentiated liposarcoma.

Elastofibroma Dorsi: Clinicopathological Analysis of 76 Cases

Background We aimed to investigate the epidemiological, clinical, paraclinical, and treatment aspects of elastofibroma dorsi through a retrospective study of 76 patients who underwent surgery between January 2008 and December 2012 in our department. Methods Our study is retrospective between January 2008 and December 2012. We admitted 79 patients with a subscapular mass, and only 76 patients had ED. The others (n=2) had high associated risk of anesthesia and were managed by a medical treatment and one patient had a subscapular sclerotic hemangioma. Results The average age of the patients was 49 years (range, 38 to 70 years), with a female predominance (54 females and 22 males). Subscapular location was constant. The right, left, and bilateral form was noted in 41, 15 and 20 cases, respectively. The diagnosis was clinical in 60 cases. Ultrasound and computerized tomography scans confirmed the diagnosis of an ill-defined mass in a subscapular location in all cases. Surgical treatment consisted of complete resection of the mass. The clinical diameter of the mass remained significantly lower than that of the surgical specimen (7 cm versus 12 cm) because the major hidden part of the mass in the subscapular area was inaccessible to palpation. Complications were noted in 9 cases (11.8%), seroma in 8 cases (10.5%), infection of wound site in 4 cases (5%), and parietal textilome in one case (1%). No case of recurrence was noted. Conclusion Surgery of elastofibroma is unique because of the subscapular location of the parietal tumor, whose histological fibrous nature makes it very adherent to the chest wall.

Incidents and complications of permanent venous central access systems: a series of 1,460 cases.

Background Implanted venous access devices or permanent central venous access systems (PCVASs) are routinely used in oncologic patients. Complications can occur during the implantation or use of such devices. We describe such complications of the PCVAS and their management. Methods Our retrospective study included 1,460 cases in which PCVAS was implanted in the 11 years between January 2002 and January 2013, including 810 women and 650 men with an average age of 45.2 years. We used polyurethane or silicone catheters. The site of insertion and the surgical or percutaneous procedure were selected on the basis of clinical data and disease information. The subclavian and cephalic veins were our most common sites of insertion. Results About 1,100 cases (75%) underwent surgery by training surgeons and 360 patients by expert surgeons. Perioperative incidents occurred in 33% and 12% of these patients, respectively. Incidents (28%) included technical difficulties (n=64), a subcutaneous hematoma (n=37), pneumothoraces (n=15), and an intrapleural catheter (n=1). Complications in the short and medium term were present in 14.2% of the cases. Distortion and rupture of the catheter (n=5) were noted in the costoclavicular area (pinch-off syndrome). There were 5 cases of catheter migration into the jugular vein (n=1), superior vena cava (n=1), and heart cavities (n=3). No patient died of PCVAS insertion or complication. Conclusion PCVAS complications should be diagnosed early and treated with probable removal of this material for preventing any life-threatening outcome associated with complicated PVCAS.

Surgery of Myasthenia Gravis Associated or Not With Thymoma: A Retrospective Study of 43 Cases

OBJECTIVES Thymectomy is a surgical treatment of myasthenia gravis. Our goal is to report our experience in the surgical treatment of myasthenia gravis with or without thymoma and a review of the literature. MATERIALS AND METHODS This is a retrospective study over a period of 10 years (2001-2010) on 43 patients: 28 women and 15 men with a mean age of 39.3 years (range 16-68 years). The myasthenia gravis was confirmed by clinical, electromyographic data and the presence of antibodies to acetylcholine receptors. RESULTS Computed tomography objectified thymic mass in 14 cases (32.5%) enlarged thymus without visible mass in eight cases (18.6%). All patients received anticholinesterase, cortico steroids in 25 cases and in three cases plasmapheresis was required. The surgical approach was total sternotomy (n=32 cases), cervicotomy (n=2), cervical and manubriotomy (n=1), a manubriotomy (n=3) and a thoracotomy in five cases (lateralised thymoma). All patients underwent a total thymectomy associated or not with resection of the tumour. Intensive Care Unit was necessary for at least 24h up to six days. The postoperative course was marked by a myasthaenic crisis (n=2) and respiratory failure (n=3) with a favourable outcome. The prognosis was marked by a complete remission in 14 cases, partial remission in 11 patients, stabilisation (n=16 cases) and increasing crisis in two patients. CONCLUSION Thymectomy certainly allows clinical improvement and reduced crisis of myasthenia gravis. Long term monitoring will confirm the benefit of non-oncological thymectomy alone or in combination with standard treatments for patients with generalised myasthenia gravis without thymoma.

L'actinomycose pulmonaire chez l'enfant

Pulmonary actinomycosis is a rare bacteriological disease, characterized by local suppuration and an extensive fibro-inflammatory process, with a possible pseudotumoral outcome. We report on a case in a 15-year-old boy, admitted in our department for prolonged pleuropneumopathy. Clinical and radiological findings were not contributive. The diagnosis of actinomycosis was obtained by pathology after surgical resection. This disease can mimic on lung X-rays a number of disorders, such as pulmonary tuberculoma, invasive tuberculosis or lung carcinoma. Pleuropulmonary actinomycosis is a rare intrathoracic infection during childhood, of which poor outcome and tough diagnosis lead usually to a surgical attitude given a picture of recurrent pulmonary abnormality. When the diagnosis is established, the treatment is medical.

Les kystes hydatiques thoraciques extrapulmonaires

Resume Objectif Rapporter notre experience dans l’approche diagnostique et therapeutique des kystes hydatiques thoraciques extra-pulmonaires, tout en soulignant les aspects etiopathogeniques de l’affection. Patients et methodes Sur 80 patients operes dans notre service pour kyste hydatique thoracique entre septembre 2001 et septembre 2005, 6 (7,5 %) avaient une localisation extra-pulmonaire, dont une multiple. Il s’agissait de 4 hommes et 2 femmes, avec un âge moyen de 43 ans. Les sites atteints etaient la plevre, le mediastin et le diaphragme. Tous les patients ont ete operes par thoracotomie et la confirmation diagnostique etait per-operatoire. Resultats Un patient avait une localisation multiple (diaphragme, mediastin anterieur et plevre). Le kyste etait intact chez 5 malades et rompu chez 1 malade. Le diagnostic etait suspecte en pre-operatoire et confirme en per-operatoire. Les suites operatoires etaient simples dans tous les cas. Aucune recidive n’a ete observee durant la periode du suivi post-operatoire. Conclusion La localisation thoracique extra-pulmonaire du kyste hydatique est une entite rare, meme dans un pays de forte endemie. Une prise en charge precoce evite la survenue de complications potentiellement fatales. La chirurgie est le traitement de choix. Le traitement medical est reserve aux formes compliquees.

Primary mediastinal goiters

BackgroundPrimary mediastinal goiters (PMG) are very uncommon; few cases were reported in the literature.Patient descriptionWe report here two cases of mediastinal goiters that met all criteria of PMG. Transternal approach was necessary for complete removal and pathological diagnoses confirmed their adenomatous goiter nature. The rarity of their occurrence, their clinical characteristics and surgical management were discussed.ConclusionPMG is part of the differential diagnoses of mediastinal masses. Safe excision is ensured through transthoracic approach.