Jesper Dammeyer

Psychosocial Development in a Danish Population of Children With Cochlear Implants and Deaf and Hard-of-Hearing Children

Research has shown a prevalence of psychosocial difficulties ranging from about 20% to 50% among children with hearing loss. This study evaluates the prevalence of psychosocial difficulties in a Danish population in relation to different explanatory variables. Five scales and questionnaires measuring sign language, spoken language, hearing abilities, and psychosocial difficulties were given to 334 children with hearing loss. Results show that the prevalence of psychosocial difficulties was 3.7 times greater compared with a group of hearing children. In the group of children with additional disabilities, the prevalence was 3 times greater compared with children without additional disabilities. If sign language and/or oral language abilities are good, the children do not have a substantially higher level of psychosocial difficulties than do hearing children. This study documents the importance of communication-no matter the modality or degree of hearing loss-for the psychosocial well-being of hearing-impaired children.

Prevalence and aetiology of congenitally deafblind people in Denmark.

Abstract A study of prevalence and aetiology was performed on 63 children and 127 adults in Denmark with congenital deafblindness. Using a Scandinavian definition of deafblindness, the prevalence of congenital deafblindness was found to be 1:29 000. Thirty-five different aetiological causes of deafblindness were found. Causes of congenital deafblindness were different among adults compared to causes among children. Rubella syndrome (28%, n = 36) and Down syndrome (8%. n = 10) were the largest groups among people above 18 years of age. Among children CHARGE syndrome (16%, n = 13) was the largest group. Ethnicity was also evaluated. Among children 72% were Danish, but among the adults 98% were Danish. Implications of difference in aetiology and ethnicity are discussed in relation to the Scandinavian traditions of clinical practice and identification of congenital deafblindness. Sumario Se llevó a cabo un estudio de prevalencia y etiología en 63 niños y 127 adultos con sordoceguera congénita en Dinamarca. Utilizando la definición escandinava de sordo-ceguera, se encontró que la prevalencia de sordo-ceguera congénita es de 1:29,000. Se encontraron 135 causas de sordo-ceguera. Las causas de sordo-ceguera congénita fueron diferentes entre los adultos comparadas con las de los niños. El síndrome de Rubeola (28% n=36) y el síndrome de Down (8% n=10) fueron los grupos más numerosos entre las personas mayores de 18 años. Entre los niños el síndrome CHARGE (16% n=13) fue el grupo más numeroso. También se evaluó la etnicidad. Del grupo de niños el 72% era daneses, mientras que el 92% de los adultos eran daneses. Se discuten las implicaciones sobre las diferencias etiológicas y étnicas en relación con las tradiciones escandinavas en la práctica clínica y la identificación de la sordo-ceguera congénita.

Mental and behavioral disorders among people with congenital deafblindness

The population of people with congenital deafblindness faces challenges concerning communication and mobility. Due to the significance of the sensory loss it is difficult to diagnose mental and behavioral disorders. This article investigates the prevalence of mental and behavioral disorders among 95 congenitally deafblind adults. Seventy-four percent were found to have a mental and/or behavioral diagnose. Mental retardation was found among 34%, psychosis among 13%. Mental and behavioral disorders, especially with symptoms of psychosis and mental retardation, are common among people with congenital deafblindness. Clinical experience is needed, as well as cross-disciplinary cooperation and specialized diagnostic methods together with a observation and intervention period in order to be able to assess and differentiate mental and behavioral symptoms from sensory deprivation in people with congenital deafblindness.

Deafblindness: A review of the literature

Background: Deafblindness or dual sensory loss is a rare condition among young people, but more frequent among older people. Deafblindness is a heterogeneous condition that varies with regard to time of onset and degree of vision and hearing impairment, as well as communication mode, medical aetiology, and number and severity of co-morbidity. Method: We conducted a comprehensive review of public health issues related to deafblindness. Results: Deafblindness often lead to barriers in language and communication, access to information and social interaction, which can lead to a number of health-related difficulties. Some of the reported consequences are a higher risk of depression, cognitive decline, developmental disorder in children and psychological distress. Conclusions: Deafblindness is associated with a number of health-related issues and more knowledge is needed about the impact of dual sensory loss to be able to offer the best support.

Development and characteristics of children with Usher syndrome and CHARGE syndrome

OBJECTIVE Individuals with Usher syndrome or CHARGE syndrome are faced with a number of difficulties concerning hearing, vision, balance, and language development. The aim of the study is to describe the developmental characteristics of children with Usher syndrome and CHARGE syndrome, respectively. METHOD Data about the developmental characteristics of 26 children with Usher syndrome and 17 children with CHARGE syndrome was obtained. Associations between deafblindness (dual sensory loss), motor development (age of walking), language abilities, and intellectual outcome of these children were explored for each group independently. RESULTS Both groups of children face a number of difficulties associated with vision, hearing, language, balance and intellectual outcome. Intellectual disability and/or language delay was found among 42% of the children with Usher syndrome and among 82% of the children with CHARGE syndrome. Intellectual disability was associated with language delay and age of walking for both groups. CONCLUSIONS Even though Usher and CHARGE are two different genetic syndromes, both groups are challenged with a number of similar developmental delays. Clinicians need to be aware of several developmental issues in order to offer adequate support to children with Usher or CHARGE syndrome.

Measure of Node Similarity in Multilayer Networks.

The weight of links in a network is often related to the similarity of the nodes. Here, we introduce a simple tunable measure for analysing the similarity of nodes across different link weights. In particular, we use the measure to analyze homophily in a group of 659 freshman students at a large university. Our analysis is based on data obtained using smartphones equipped with custom data collection software, complemented by questionnaire-based data. The network of social contacts is represented as a weighted multilayer network constructed from different channels of telecommunication as well as data on face-to-face contacts. We find that even strongly connected individuals are not more similar with respect to basic personality traits than randomly chosen pairs of individuals. In contrast, several socio-demographics variables have a significant degree of similarity. We further observe that similarity might be present in one layer of the multilayer network and simultaneously be absent in the other layers. For a variable such as gender, our measure reveals a transition from similarity between nodes connected with links of relatively low weight to dis-similarity for the nodes connected by the strongest links. We finally analyze the overlap between layers in the network for different levels of acquaintanceships.

Disability as a risk factor? Development of psychopathology in children with disabilities

Empirical research has established that children with disabilities are more likely to develop psychopathology than children without disabilities. But too little is known about the association between disability and psychopathology. The aim of this article is to discuss developmental psychopathological models that conceptualise the connection between childhood disability and psychopathology. Empirical studies of psychopathology among children with a congenital hearing impairment and children with cerebral palsy will be reviewed, representing in-depth examples of association between disability and psychopathology. Both a congenital hearing impairment and cerebral palsy were found to be dominating risk factors for all types of psychopathology, but no relationship was identified between degree of disability and risk of psychopathology. The higher risk cannot be explained by biological impairments alone. To explain the contradictory findings, developmental models of disability and psychopathology are applied. Within a multi-factorial developmental psychopathological perspective and a dialectical model of disability (Vygotsky, 1993), it is suggested that disability can be understood as an incongruence between the individual development of the child and demands and expectations in the specific relations and institutions in which the child participates. This incongruence creates and strengthens negative factors for the child with disability and results in a higher risk of psychopathology.

Disability as a Dialectical Concept: Building on Vygotsky's Defectology

The legacy of defectology, Vygotsky’s theoretical work on children with disabilities, still offers a useful approach in disability research. Vygotsky understood disability as an incongruence between the individual’s psychological structure and the structure of cultural forms. The incongruence describes a dialectical relation between the person with a disability and the surrounding society. The aim of this study is to explore Vygotsky’s concept of incongruence. A case example is presented. Through video observation of a child with severe cerebral palsy (CP) and cognitive visual impairment, the incongruence is analysed in two settings: in school together with a teacher and at home together with his mother. Use of vision, arm movement and a Rolltalk (a computer for communication) were the categories selected for analysis. The results demonstrate how the impact of the boy’s cognitive visual impairment and CP differed depending on the interaction with the environment and on how his teacher and mother interacted with him. The dialectical dynamics of incongruence in each of the two settings created different levels of abilities/disabilities. It is argued that the dialectical psychological understanding of disability offers a useful approach to overcome dualistic understandings of the person with a disability and the surrounding society.

Children with Usher syndrome: mental and behavioral disorders

BackgroundMental and behavioral disorders among adults with Usher syndrome have been discussed and reported in some case studies but no research has been reported on children with Usher syndrome.MethodsThis article investigates the prevalence and characteristics of mental and behavioral disorders among 26 children, 3-17 years of age, with Usher syndrome.ResultsSix of the 26 children were diagnosed with a mental or behavioral disorder (1 with schizophrenia and mild mental retardation, 1 with atypical autism and severe mental retardation, 1 with atypical autism and mild mental retardation, 1 with mild mental retardation, and 2 with conduct disorder). Another 3 children had had a mental or behavioral disorder previously in their childhood.ConclusionEven though vision impairment first manifests in late childhood, some children with Usher syndrome seem to develop mental and behavioral disorders during childhood. The aetiology and treatment of mental and behavioral disorders among children with Usher syndrome are discussed. Children with Usher syndrome and their parents may need clinical support during early childhood to prevent development of mental and behavioral disorders.

Symptoms of Autism among Children with Congenital Deafblindness.

Associations between congenital deafness or blindness and autism have been found. The main consequences of congenital sensory impairment, being barriers for communication, language and social interaction development, may lead to symptoms of autism. To date only few studies have been reported concerning individuals with congenital deafblindness. This study examines symptoms of autism among 71 children with congenital deafblindness using the Autism Behavior Checklist. The cohort of children with congenital deafblindness was found to have symptoms of autism on a level similar to children with another developmental disorder than autism for example intellectual disability. No association was found between severity of congenital sensory impairment and severity or type of symptoms of autism.