Mohammed Azfar Siddiqui

Atypical multifocal hydatid disease of cranial vault: simultaneous orbital and extradural meningeal involvement.

Hydatid disease is endemic in regions where livestock is raised. Liver and lungs are the most commonly affected organs by the disease. Cranial vault and orbital hydatid disease is extremely rare. Signs and symptoms along with serological investigation are often inconclusive in cranial hydatid, making radiological diagnosis extremely important. Surgical removal of the cyst is the mainstay of treatment. Postoperative medical therapy, along with regular follow-up, is the key to detect any recurrence. We report an unusual case of cranial hydatid which showed diffuse scalp infiltration along with oribital and extradural extension.

Bilateral Persistent Hyperplastic Primary Vitreous: A Close Mimic of Retinoblastoma

Bilateral persistent hyperplastic primary vitreous (PHPV) is a rare disorder of eye. It is one of the most important differential diagnoses of retinoblastoma, hence early and accurate diagnosis is important. We here report a case of an 11-month-old child which was referred to ocular OPD with complaints of bilateral leukocoria. Examination revealed greyish-white masses posterior to both lenses, raising the clinical suspicion of retinoblastoma. Ultrasonography demonstrated echogenic masses extending from the posterior surface of the lens to the optic disc with reduced axial lengths. These masses demonstrated flow on color Doppler evaluation. CT scan revealed hyperdense masses behind the lens without any evidence of intralesional calcification. Clinical features and imaging findings point towards the diagnosis of bilateral PHPV. PHPV is a developmental disorder of the globe in which the hyaloid vasculature fails to regress normally. While unilateral PHPV is common, bilateral PHPV is a rare entity. It is one of the most important conditions mimicking retinoblastoma; hence early and accurate diagnosis is required. Ophthalmological examination is still the best way to confirm the diagnosis. However, if the diagnosis remain unclear, further evaluation using ultrasonography, Color Doppler, and CT scan is useful.

Isolated tubercular scaphoid osteomyelitis: a case report

Bone is the third most frequent site of tuberculosis after lung and lymph node, accounting for 10%–20% of all cases of extrapulmonary disease. The spine and hip are the most commonly involved sites. Involvement of the small bones of the hand has been described exceedingly rarely, and is usually secondary to pulmonary disease. Because a primary focus is not always found, it can be difficult to make a diagnosis of skeletal tuberculosis. Moreover, because clinical and radiographic features are nonspecific, an early diagnosis will only be made where there is a high degree of suspicion. Isolated osteomyelitis of the scaphoid is uncommon, having previously been reported in association with animal bites and interventions such as radial artery cannulation. We describe here the unusual occurrence of tubercular osteomyelitis of the scaphoid, a condition which has rarely been reported.

A case report: Urinoma as initial presenting sign of bladder malignancy

Indian Journal of Cancer | October-December 2011 | Volume 48 | Issue 4 50% in the vagina, whereas, the vulva and corpus are extremely rare sites.[1] The clinical presentation includes a history of bloody vaginal discharge, often accompanied by a polypoid mass protruding from the vagina. Pervaginal examination, best performed under anesthesia, demonstrates a lesion that is polypoid and friable arising from the vagina or cervix. With this clinical presentation it is not surprising that many are clinically misdiagnosed as sarcoma botryoides (embryonal rhabdomyosarcoma).

Schwannoma of the scrotum: case report and review of the literature.

Schwannomas are benign nerve sheath tumors composed of Schwann cells, which normally produce the insulating myelin sheath covering the peripheral nerves. Common locations include the head, neck, mediastinum, and retroperitoneum. These tumors are usually asymptomatic until they become large and compress the surrounding tissues. Most schwannomas occur during the third and fourth decades of life, with an equal gender distribution. We present the case of a schwannoma that originated in the scrotum.

Hydatid cyst in tail of pancreas

The authors present a case of hydatid cyst in tail of pancreas in a 35-year-male who presented with 6-month history of dull aching pain in abdomen. Radiologically, a differential diagnosis of cystic pancreatic neoplasm and pseudocyst was made which was confirmed after histopathological examination.

Ameloblastic carcinoma: a rare entity

Ameloblastic carcinoma is a rare aggressive malignant epithelial odontogenic tumour seen in a wide range of age group with no sex predilection. Patient usually presents with a rapidly enlarging swelling. It usually involves the posterior portion of the mandible. Treatment of choice is surgical removal of tumour followed by radiotherapy. We present a case of ameloblastic carcinoma in a 35-year-old man.

Neurocutaneous melanosis: Review of a rare non-familial neuroectodermal dysplasia with newer association of cerebellopontine angle cistern lipoma

Neurocutaneous melanosis is a rare neuroectodermal dysplasia with a grave prognosis. It is actually a disorder of neuronal migration at the time of the embryogenesis hence classified as a neurocristopathy. The patients are initially identified by the skin manifestations of the disease in the form of melanocytic naevus which can be hairy or non-hairy. These patients may or may not present with neurological symptoms but often show CNS abnormalities especially on MRI of the brain and the spine. A lot has been described about the disease since the first case described by Rokitansky in 1861, but every time a new CNS pathology is being added to the long list of currently documented pathologies. Herein we describe a case of a 5 yr old boy with seizures and hairy melanocytic naevus over the trunk and back who was diagnosed as a case of Neurocutaneous melanosis on subsequent evaluation by CT and MRI. We also describe the new association of CP angle cistern lipoma with neurocutaneous melanosis.

Ewing's sarcoma of scapula: a rare entity

Ewings sarcoma is the second most common malignant bone tumour of childhood and adolescence. It may affect any bone, but it is frequent in the femur, ilium and the tibia. Here the authors are reporting a case of Ewings sarcoma involving scapula in a 14-year-old boy presenting with pain and swelling around the shoulder. Swelling was removed which on histopathological examination showed solid sheets closely packed, poorly differentiated small cells that have a high nuclear-cytoplasmic ratio, fine chromatin and small nucleoli. A tentative diagnosis of Ewings sarcoma was made which was confirmed by immunohistochemistry.

Extreme Ophthalmomyiasis externa with simultaneous facial and scalp involvement

BACKGROUND Ophthalmomyiasis is a rare entity seen mainly in immunocompromised host with neglected wounds under poor hygienic conditions. CASE We report a case of extreme ophthalmomyiasis with extensive facial and scalp involvement in an old rural inhabitant following evisceration. CONCLUSION Proper wound care and personal hygiene are of paramount importance for good wound healing.