Oscar Bianchi

Chronic Benign Familial Pemphigus

ABSTRACT Ten patients with benign familial chronic pemphigus (BFCP) (Hailey‐Hailey disease) were evaluated; semio‐logic and localization differences were described, and special attention was given to solitary or atypical forms. In all the cases, the diagnosis was confirmed by histopathology; some histopathologic differences and the results achieved by direct irnmunofluorescence of skin are discussed. Most of the patients responded to the treatment with corticosteroids and antibiotics.

Hereditary complement (C2) deficiency with discoid lupus erythematosus and idiopathic atrophoderma.

ABSTRACT. A Family with hereditary deficiency of the second component of complement was studied. Three siblings were homozygous for C2 deficiency and two of them had associated skin diseases. Ono sister presented with idiopathic atrophoderma and the other had clinical and pathological manifestations of discoid lupus erythematosus. This is the first description of an association between idiopathic atrophoderma and C2 deficient state.

Ectopic Geographic Tongue and AIDS

A 23–year‐old man with AIDS developed a lesion with the clinical characteristics of an ectopic geographic tongue in the lower lip, near the right commissure.