Hye Kyung Yoon

Intramuscular vascular malformations of an extremity: findings on MR imaging and pathologic correlation.

Abstract Objective. To analyze the findings of intramuscular vascular malformations of an extremity on MR imaging and to correlate these findings with histopathologic examination. Design and patients. The findings on MR imaging and the medical records of 14 patients with an intramuscular vascular malformation of the extremity were retrospectively studied. All patients underwent surgical excision. Diagnoses were based on the results of pathologic examination. Findings on MR imaging were noted and correlated with the histopathologic findings. Results. Intramuscular vascular malformations of an extremity showed multi-septate, honeycomb, or mixed appearance on MR imaging. Multi-septate areas correlated with dilated and communicating vascular spaces with flattened endothelium. Honeycomb areas corresponded to vascular spaces with inconspicuous small lumina and thickened vascular walls. Areas of increased signal intensity on T2-weighted images were found in all intramuscular vascular malformations. Infiltrative margins were more commonly seen in intramuscular lymphaticovenous malformations. Adherence to neurovascular structures and orientation of the lesion along the long axis of the affected muscle were more commonly seen in intramuscular venous malformations. Conclusions. Intramuscular vascular malformations showed either a multi-septate, honeycomb, or mixed appearance, reflecting the size of the vascular spaces and the thickness of the smooth muscles of the vessel walls. Prediction of the subtype of an intramuscular vascular malformation of an extremity on MR imaging seems to be difficult, although there are associated findings that may be helpful in the differential diagnosis of each subtype.

Imaging Findings of Osler-Weber-Rendu Disease Involving the Liver

Osler -Weber -Rendu disease or hereditary hemorrhagic telangiectasia(HHT) has been known to be an autosomal dominant disorder characterized by telangiectases and arteriovenous malformations of multiple organ systems(1). Hepatic involvement occurs in 8-31 % ofcases with HHTand includes telangiectases or arteriovenous fistulas associated with fibrosis and cirrhosis(2 , 3). Recent reports demonstrate various imaging findings including Doppler sonography with color flow signals , CT, and MR findings of the liver involvement in patients with HHT(2 -4). A few cases with HHT had reported in Korea(5). We describe the findings of conventional and Doppler sonography, and computed tomogram(CT) in a case with HHT involving the liver