Angus C Cameron

A case of neurocristopathy that manifests facial clefting and maxillary duplication

A case of a 6-year-old child with three facial clefts and maxillary duplication is presented. Computerized three-dimensional reconstruction from computerized tomography imaging was used in the diagnosis of this patient, and an explanation of the possible embryologic causes of this malformation is discussed.

Hereditary Mucoepithelial Dysplasia

Abstract: We report an individual with the rare autosomal recessive condition known as hereditary mucoepithelial dysplasia. The diagnosis was based on clinical features and characteristic ultrastructural changes in oral mucosal biopsy specimens.

KBG syndrome: review of the literature and findings of 5 affected patients

KBG syndrome is a rare, multiple congenital anomaly/mental retardation (MCA/MR) syndrome characterized by neurological disturbance, short stature, a distinct craniofacial appearance, and skeletal anomalies. It is likely to be autosomal dominant in nature with a wide range of expressivity in its clinical features. Dentally, macrodontia, particularly of the maxillary permanent central incisors is a common finding. The aim of this article was to review the familiar clinical presentations of this syndrome and to highlight previously unreported findings of generalized macrodontia and shovel-shaped incisors. Dental and clinical findings of 2 affected brothers with a 3-year follow-up of their dental progress following orthodontic treatment are outlined. Additionally, dental and clinical findings of an affected mother and her daughter, and another sporadic case are also presented.

7 – Pulp therapy for primary and immature permanent teeth

Methods Recommendations on pulp therapy for primary and immature permanent teeth were developed by the Clinical Affairs Committee – Pulp Therapy Subcommittee and adopted in 1991. This document by the Council of Clinical Affairs is a revision of the previous version, last revised in 2009. This revision included a new systematic literature search of the PubMed®/MEDLINE database using the terms: pulpotomy, pulpectomy, indirect pulp treatment, stepwise excavation, pulp therapy, pulp capping, pulp exposure, bases, liners, calcium hydroxide, formocresol, ferric sulfate, glass ionomer, mineral trioxide aggregate (MTA), bacterial microleakage under restorations, dentin bonding agents, resin modified glass ionomers, and endodontic irrigants; fields: all. Papers for review were chosen from the resultant lists and from hand searches. When data did not appear sufficient or were inconclusive, recommendations were based upon expert and/or consensus opinion including those from the 2007 joint symposium of the AAPD and the American Association of Endodontists (AAE) titled Emerging Science in Pulp Therapy: New Insights into Dilemmas and Controversies (Chicago, Ill.)